PAH

HIV Viral Loads May Affect Echocardiographic Pulmonary Pressure
December 05, 2017Individuals who are HIV-positive may be at a higher risk for increased pulmonary pressure and mortality.

Anticoagulation Therapy Often Poorly Managed in Pulmonary Arterial Hypertension
December 04, 2017A study evaluated the quality of targeted anticoagulation in patients with PAH, and examined outcomes associated with poor time spent within targeted anticoagulation range.

Lung Transplantation for Pulmonary Arterial Hypertension: Overview and Bridging Therapies
November 30, 2017Lung transplantation may be an option in patients with severe pulmonary arterial hypertension who do not respond well to medical therapy.

Riociguat Studied in Pediatric Patient With Pulmonary Arterial Hypertension
November 30, 2017Select pediatric patients with pulmonary arterial hypertension may benefit from treatment with riociguat.

Pulmonary Arterial Hypertension: Mechanisms of Exercise Intolerance
November 08, 2017Respiratory muscle dysfunction, iron deficiency, and skeletal muscle dysfunction have been implicated as mechanisms for exercise intolerance in pulmonary arterial hypertension.

Redesigned Inhalation Device for PAH Approved by FDA
November 02, 2017The new device features a more ergonomic design with a single-button operation, an intuitive user interface to adjust breath counts, a rechargeable battery, and a display that guides patients through the inhalation process.

Phenotypes Associated With EIF2AK4 Mutations in PAH
November 02, 2017The frequency of eukaryotic translation initiation factor 2 alpha kinase 4 gene (EIF2AK4) mutations in patients with pulmonary arterial hypertension was investigated.

Pulmonary Edema After Prostacyclin Therapy for PAH Associated With Worse Outcomes
November 01, 2017Patients who develop pulmonary edema after starting prostacyclin for pulmonary arterial hypertension have a greater risk for mortality.

PAH-Associated Congenital Heart Disease Outcomes Predicted by Pulmonary Artery Compliance
November 01, 2017Pulmonary vascular compliance may independently predict survival and prognosis in patients with pulmonary arterial hypertension associated with congenital heart disease.

Pulmonary Arterial Compliance Improved With Riociguat vs PDE5 Inhibitors
November 01, 2017Patients with pulmonary arterial hypertension experienced better improvements in pulmonary arterial compliance with riociguat compared with phosphodiesterase type 5 inhibitors.

Extent of Right Ventricular Epicardial Vascularization in Pulmonary Arterial Hypertension
October 31, 2017Right ventricular epicardial vasculature is more extensive in patients with pulmonary arterial hypertension compared with individuals without disease.

No Associations Exist Between 6MWD and Maximum Oxygen Uptake in Pulmonary Arterial Hypertension
October 29, 2017Results indicate that further study of the relationship between the 6-minute walk distance test and functional capacity in PAH is necessary.

Survival Rates in Eisenmenger Syndrome Treated With Pulmonary Vasodilator Therapy
September 22, 2017Patients undergoing pulmonary vasodilatory therapy were more functional at initial presentation.