Obstructive Lung Disease

Is There an “Ideal” Cystic Fibrosis Candidate for Lung Transplantation?

By

Suzanne Bujara

Publish Date August 23, 2018

Lung transplantation can extend survival in patients with cystic fibrosis who have compromised lung function and increasing exacerbations.

Mannitol Inhalation Powder Now Available as Add-On Maintenance Therapy for Cystic Fibrosis

By

Diana Ernst, RPh

Publish Date April 6, 2021

Bronchitol should only be used by adults who have passed the Bronchitol Tolerance Test.

Telehealth for Cystic Fibrosis During COVID-19 Largely Accepted by Clinicians

By

Brandon May

Publish Date March 25, 2021

Clinicians across multiple disciplines largely accepted telehealth in the cystic fibrosis care model during the COVID-19 pandemic.

Elexacaftor-Tezacaftor-Ivacaftor Associated With Rapid Improvement in Cystic Fibrosis

By

Virginia A. Schad, PharmD, RPh

Publish Date March 19, 2021

In patients with cystic fibrosis with advanced lung disease, initiation of elexacaftor-tezacaftor-ivacaftor is associated with rapid clinical improvement and a decreased need for lung transplantation.

Hormonal Contraception May Have Beneficial Effects for Women With Cystic Fibrosis

By

Bryant Moeller

Publish Date February 23, 2021

Women with cystic fibrosis have inflammatory biomarker fluctuations in the lungs that correlate with changes in lung function, opening the possibility of sex hormone linked changes.

FDA Expands Use of Multiple Cystic Fibrosis Medications

By

Brian Park, PharmD

Publish Date December 29, 2020

The full list of CFTR gene mutations for Trikafta, Symdeko and Kalydeco can be found in the updated prescribing information for each respective product.

Vitamin D Deficiency is Associated With NTM in Cystic Fibrosis

By

Virginia A. Schad, PharmD, RPh

Publish Date December 18, 2020

Vitamin D deficiency is associated with a higher risk of incident nontuberculous mycobacteria respiratory isolation in adults with cystic fibrosis.

Mannitol Approved as Add-On Maintenance Therapy for Cystic Fibrosis

By

Brian Park, PharmD

Publish Date November 9, 2020

Bronchitol is only indicated for use in adults who have passed the Bronchitol Tolerance Test.

Ivacaftor May Be Effective for Infants With Cystic Fibrosis and Gating Mutation

By

Brandon May

Publish Date November 2, 2020

Ivacaftor was safe and associated with improvements in cystic fibrosis transmembrane conductance regulator function in infants with CF and a gating mutation.